Familial exudative vitreoretinopathy: an overview

Abstract

Familial exudative vitreoretinopathy (FEVR) is a rare inherited disorder, characterised by the abnormal development of retinal blood vessels. FEVR is marked by an avascular peripheral retina, which may give rise to a range of sight-threatening complications depending on the severity of the  disease. FEVR and retinopathy of prematurity almost share the same ocular manifestations, but most FEVR cases are full-term.